Nursing care in Rett Syndrome. Systematic review [Cuidado de enfermería en el Síndrome de Rett. Revisión sistemática]
DOI:
https://doi.org/10.62574/c5hahw87Keywords:
Rett Syndrome, Genes X-Linked, Cromosoma XAbstract
Objective: to analyse nursing care in Rett Syndrome. Method: Systematic review of 15 articles. Results and conclusion: specialised nursing care requires a comprehensive approach that addresses five main areas: respiratory management, nutrition and feeding, prevention of orthopaedic complications, alternative communication and psychosocial support for carers. Specialised nursing interventions can significantly improve the quality of life of patients with RS and reduce the burden on carers.
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Copyright (c) 2024 Nicole Pamela Nuñez-Nuñez, Evelyn Estefanía Guachambala-Masaquiza, Nayely Monserrath Melena-Macas, Michael Alexander Coronel-Pilataxi
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